Intrahepatic disorders Intrahepatic cholestasis persistent Idiopathic"neonatal hepatitis Alagille syndrome(arteriohepatic dysplasia) Intrahepatic biliary hypoplasia or paucity of intrahepatic bile ducts(nonsyndromic) Progressive familial intrahepatic cholestasis(PFic) Intrahepatic cholestasis, recurrent Familial benign recurrent cholestasis associated with lymphedema(Aagenaes) Congenital hepatic fibrosis Caroli disease(cystic dilatation of intrahepatic ducts)Intrahepatic disorders ◼ Intrahepatic cholestasis, persistent ◼ “Idiopathic” neonatal hepatitis ◼ Alagille syndrome (Arteriohepatic dysplasia) ◼ Intrahepatic biliary hypoplasia or paucity of intrahepatic bile ducts (nonsyndromic) ◼ Progressive familial intrahepatic cholestasis (PFIC) ◼ Intrahepatic cholestasis, recurrent ◼ Familial benign recurrent cholestasis associated with lymphedema (Aagenaes) ◼ Congenital hepatic fibrosis ◼ Caroli disease (cystic dilatation of intrahepatic ducts)