Transmissible Spongiform Encephalopathies(Prion Diseases Human Kuru disease Creutzfeldt-Jacob disease(CJD) variant Creutzfeldt-Jacob disease VCD · Anima|s Scrapie of sheep and goats Bovine spongiform encephalopathy (bse, mad cow) Progressive neurodegenerative diseaseTransmissible Spongiform Encephalopathies (Prion Diseases) • Human – Kuru disease – Creutzfeldt--Jacob disease (CJD) – variant Creutzfeldt--Jacob disease (vCJD) • Animals – Scrapie of sheep and goats – Bovine spongiform encephalopathy (BSE, mad cow) Progressive neurodegenerative disease