Phenylketonuria, PKU I Protein MIM261600 Phe PA升T Infants with PKU have a mousy odor Phenylypruvic 2. Infants with pku have acid fairer hair and skin 3. This disease can cause Phenyllactic Phenylacetic acid acid significant mental problems BenzophenonePhenylketonuria，PKUⅠ MIM 261600 1. Infants with PKU have a mousy odor PAH Phenyllactic acid Benzophenone Phe Protein Tyr Phenylypruvic acid Phenylacetic acid × 2. Infants with PKU have fairer hair and skin 3. This disease can cause significant mental problems