Vision loss Often be found at 5-10 vears old a visual acuity usually >20/100 a central visual acuity often significantly different between the two eyes a the infant may present with nystagmus or strabismus, due to the large size of the associated visual field defectVision loss ◼ Often be found at 5-10 years old ◼ visual acuity usually >20/100 ◼ central visual acuity often significantly different between the two eyes ◼ the infant may present with nystagmus or strabismus, due to the large size of the associated visual field defect